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Synonyms: rudimentary ear,
supernumery pinna, wattle, accessory auricle anomaly,
preauricular skin tag;
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Accessory tragus
is the most common congenital defect of the external ear.
In the vast majority of cases it is an isolated developmental
defect not associated with other abnormalities.
It is linked to maldevelopment of the first and second
branchial arches.
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Etiology: 1). isolated (non-syndromal);
2). Associated with
4p-
syndrome (Wolf-Hirschhorn syndrome),
Simpson-Golabi-Behmel syndrome or
facio-auriculo-vertebral syndrome (Goldenhar syndrome);
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Gross: often present in a
pre-auricular location, but may appear anywhere along the path
to the corner of the mouth, or more rarely, over the
sternocleidomastoid muscle;
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Histology: a polypoid structure
containing skin, hair, fibroadipose tissue and cartilage. It is
otherwise unremarkable;
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Differential diagnosis: This
lesion may be confused with a fibroepithelial polyp
(acrochordon) or soft fibroma, but the anatomic location and the
presence of vellus follicles and cartilage leads to the correct
designation.
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