-
Mostly inguinal lymph node,
solitary and painless
-
Benign, rarely recurs
-
Micro:
-
Palisading spindle
cells, no nuclear atypia, rare mitoses
-
Amianthoid bodies:
homogeneous eosinophilic collagen deposit, fine hair-like
spokes, peripheral granular weakly eosinophilic area. Trichrome
stain +
-
Hemorrhage,
hemosiderin deposit
-
IPX: SMA+, myosin+,
vimentin+; desmin-, Factor VIII -, S100-, synaptophysin-
-
DDX:
-
Kaposi sarcoma: no
Amianthoid bodies, but shows endothelial clefts, RBC
extravasculation, inflammatory cells, and HHV8+
-
Schwannoma: no
Amianthoid bodies, but shows Antoni A and B patterns,
thick-walled vessels, and S100+
-
Spindle cell sarcoma:
atypia, mitosis and lack of Amianthoid bodies
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