Gene Translocations In Leukemia And Lymphoma

 

 

Uploaded: 2007-12-07, Updated: 2007-12-07

 

Tumor

Translocation

 Fused Gene

Anaplastic large cell lymphoma t(2;5)(p23;q35) 70-80% NPM-ALK
t(1;2)(q25;p23) 20% TPM3-ALK
Burkitt's lymphoma t(8;14)(q24;q32) 60-70% IgH-cMYC
t(8;22)(q24;q11) 10-15% IgL-cMYC
t(2;8)(p12;q24) 2-5% IgK-cMYC
Follicular lymphoma t(14;18)(q32;q21) 80-90% IgH-BCL2
t(2;18)( p11;q21)   IgL-BCL2
t(18;22(q21;q11)   IgK-BCL2
Lymphoplasmacytic lymphoma t(9;14)(p13;q32) 50% IgH-PAX5
Mantle cell lymphoma t(11;14)(q13;q32) 50-70% IgH-BCL1
MALT lymphoma/marginal zone lymphoma t(11;18)(q21;q21) 20-50% API2-MLT
t(14;18)(q32;q21) 10-20% IgH-MLT1
t(1;14)(p22;q32) 5-10% IgH-BCL10
t(3;14)(p14;q32) 10% IgH-FOXP1
Acute promyelocytic leukemia t(15;17)(q22;q12) 98% PML-RARA
Chronic myelogenous leukemia t(9;22)(q34;q11) 100% BCR-ABL
       
 
     
List of Genes Involved in Translocation

Gene

Aliases

Location

Function

ALK

2p23

Membrane associated TKR; probable role in the nervous system development and maintenance

TPM3

NEM1

1q25

Actin-binding proteins, component of cytoskeletal microfilaments; mediate the effect of Ca2+ on the myosin-actin interaction

NPM1

NPM

5q35

RNA binding nucleolar phosphoprotein, involved in preribosomal assembly; transport ribonucleoproteins between cellular compartments

C-MYC

8q24

b-HLH-Zip transcription factor, activate transcription and promote cell proliferation and transformation

BCL2

18q21

Antiapoptosis by forming complexes with caspase-9 and APAF1

IgH

14q32.33

Immunoglobulin heavy chains

BCL1

Cyclin D1

11q13

Role in the cell cycle control, G1 progression and G1/S transition

PAX5

BSAP

9p13

Required for B cell lineage commitment during early B cell development and also for B lineage maintenance

BIRC3

API2

11q21

Member of the 'inhibitor of apoptosis' (IAP) protein family. Binds to the tumor necrosis factor receptor via its associated factors TRAF1 and TRAF2 and inhibits apoptosis, probably by interfering with activation of caspaces.

MALT1

MLT

18q21

BCL10

CARMEN

1p22

A caspase recruitment domain; role in the apoptosis

FOXP1

QRF1

3p14.1

Transcription factor; member of the FOXP subfamily, characterized by a DNA binding forkhead

PML

MYL

15q22

Nuclear protein; contains zinc fingers and a leucine zipper; transcription factor.

RARA

 

17q12-21

Nuclear receptor; binds HRE, igand and dimerization domain; role in growth and differentiation.

ABL

ABL1

9q34

Nuclear c-ABL plays a major role in the regulation of cell death after DNA damage. Cytoplasmic c-ABL possibly functions in adhesion signaling.

BCR

PHL

22q11

Protein kinase; probable role in signal transduction

 
REFERENCES
  • http://atlasgeneticsoncology.org/